Title

Aortic root aneurysm repair in a neonate with Loeys-Dietz syndrome

Authors

Willa Li
William Cohen
Pamela Combs
Joshua Wong, Advocate Aurora HealthFollow
Rohit S. Loomba, Advocate Aurora HealthFollow
Brian K Lee, Advocate Aurora HealthFollow
Chawki Elzein, Advocate Aurora HealthFollow
Michel Ilbawi, Advocate Aurora HealthFollow
Luca Vricella, Advocate Aurora HealthFollow
Narutoshi Hibino, Advocate Aurora HealthFollow

Recommended Citation

Li W, Cohen W, Combs P, Wong J, Loomba R, Lee BK, El-Zein C, Ilbawi M, Vricella L, Hibino N. Aortic root aneurysm repair in a neonate with Loeys-Dietz syndrome. Cardiol Young. 2021 Jan 25:1-3. doi: 10.1017/S1047951120004886. Epub ahead of print. PMID: 33487195

Affiliations

Pediatric Cardiology, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiology, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiology, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiac Surgery, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiac Surgery, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiac Surgery, Advocate Children's Heart Institute, Advocate Children's Hospital

Pediatric Cardiac Surgery, Advocate Children's Heart Institute, Advocate Children's Hospital

Abstract

Loeys-Dietz syndrome is a connective tissue disorder known to cause aggressive aortopathy in paediatric patients, but it is extremely rare for cardiovascular events to present during infancy. We report the first successful aortic repair in a neonate with LDS presenting in extremis with an early onset, massive aortic aneurysm.

Document Type

Article

PubMed ID

33487195

DOI

10.1017/S1047951120004886